<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2307-0420</journal-id>
<journal-title><![CDATA[Cirugía paraguaya]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Cir. Parag.]]></abbrev-journal-title>
<issn>2307-0420</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Paraguaya de Cirugía]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2307-04202019000100041</article-id>
<article-id pub-id-type="doi">10.18004/sopaci.2019.abril.41-43</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[POLIPOSIS JUVENIL FAMILIAR EN LA INFANCIA]]></article-title>
<article-title xml:lang="en"><![CDATA[CHILDHOOD FAMILIAR JUVENILE POLIPOSIS]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fernández]]></surname>
<given-names><![CDATA[Pamela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Paredes]]></surname>
<given-names><![CDATA[Julio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rizzi]]></surname>
<given-names><![CDATA[Aurora]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vera]]></surname>
<given-names><![CDATA[Alcito]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Soskin]]></surname>
<given-names><![CDATA[Ana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Nacional de Itaugua Servicio de Anatomía Patológica ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Paraguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2019</year>
</pub-date>
<volume>43</volume>
<numero>1</numero>
<fpage>41</fpage>
<lpage>43</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_arttext&amp;pid=S2307-04202019000100041&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_abstract&amp;pid=S2307-04202019000100041&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_pdf&amp;pid=S2307-04202019000100041&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN El síndrome de poliposis juvenil es un trastorno autosómico dominante, raro y ocurre en 1 en 100.000 a 160.000 personas en la población general. Existe la forma familiar y la esporádica. El 20% al 50% de los pacientes tienen antecedentes familiares de pólipos. Los pólipos juveniles aparecen tras el primer año de vida, en su mayoría son de características benignas, sin embargo, cuando son múltiples y/o existe historia familiar de poliposis, se debe sospechar de este síndrome. El diagnóstico oportuno y el seguimiento de los pacientes conllevan a mejorar los síntomas y prevenir carcinoma colorrectal en estos grupos de riesgo. Se presentan los casos de dos hermanos con esta entidad que consultaron por sangrado rectal, cuyo tratamiento y evolución han sido favorables.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Juvenile polyposis syndrome is an autosomal dominant disorder, rare and occurs in 1 in 100,000 to 160,000 people in the general population. There is the familiar and sporadic form. 20% to 50% of patients have a family history of polyps. Juvenile polyps appear after the first year of life, they are mostly benign, however, when they are multiple and / or there is a family history of polyposis, you should suspect this syndrome. Timely diagnosis and follow-up of patients lead to improvement of symptoms and prevention of colorectal carcinoma in these risk groups. We present the cases of two brothers with this entity who consulted for rectal bleeding, whose treatment and evolution have been favorable.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Poliposis juvenil]]></kwd>
<kwd lng="es"><![CDATA[historia familiar]]></kwd>
<kwd lng="es"><![CDATA[colectomía total]]></kwd>
<kwd lng="en"><![CDATA[Juvenile polyposis]]></kwd>
<kwd lng="en"><![CDATA[family history]]></kwd>
<kwd lng="en"><![CDATA[total colectomy]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Noffsinger]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Poliposis y síndromes hereditarios de Cáncer]]></article-title>
<person-group person-group-type="editor">
<name>
<surname><![CDATA[Noffsinger]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<source><![CDATA[Fenoglio-Preiser&#8217;s Gastrointestinal Pathology]]></source>
<year>2017</year>
<edition>4ª</edition>
<publisher-loc><![CDATA[Philadelphia ]]></publisher-loc>
<publisher-name><![CDATA[Wolters Kluwer]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Chow]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Macrae]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[A review of juvenile polyposis syndrome]]></article-title>
<source><![CDATA[J Gastroenterol Hepatol]]></source>
<year>2005</year>
<numero>20</numero>
<issue>20</issue>
<page-range>1634-40</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Friedl]]></surname>
<given-names><![CDATA[W]]></given-names>
</name>
<name>
<surname><![CDATA[Kruse]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Uhlhaas]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Frequent 4-bp deletion in exon 9 of the SMAD4/MADH4 gene in familial juvenile polyposis patients]]></article-title>
<source><![CDATA[Genes Chromosomes Cancer]]></source>
<year>1999</year>
<numero>25</numero>
<issue>25</issue>
<page-range>403-6</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Brosens]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Van Hattem]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Hylind]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Iacobuzio Donahue]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Romans]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Axilbund]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Risk of colorectal cancer in juvenile polyposis]]></article-title>
<source><![CDATA[Gut]]></source>
<year>2007</year>
<numero>56</numero>
<issue>56</issue>
<page-range>965-7</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Caserras]]></surname>
<given-names><![CDATA[X]]></given-names>
</name>
<name>
<surname><![CDATA[Alvarez]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Síndrome de poliposis juvenil Boletín de actualización del Servicio de Digestivo]]></article-title>
<source><![CDATA[Hospital del Mar, Barcelona España]]></source>
<year>2010</year>
<volume>9</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>60-3</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Dahdaleh]]></surname>
<given-names><![CDATA[FS]]></given-names>
</name>
<name>
<surname><![CDATA[Carr]]></surname>
<given-names><![CDATA[JC]]></given-names>
</name>
<name>
<surname><![CDATA[Calva]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Howe]]></surname>
<given-names><![CDATA[JR]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Poliposis juvenil y otros síndromes de poliposis intestinal con microdeleciones del cromosoma 10q22-23]]></article-title>
<source><![CDATA[Clin Genet]]></source>
<year>2011</year>
<volume>81</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>110-6</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Manfredi]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Hereditary hamartomatous polyposis syndromes: understanding the disease risks as children reach adulthood]]></article-title>
<source><![CDATA[Gastroenterol Hepatol]]></source>
<year>2010</year>
<volume>6</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>185-96</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Giardiello]]></surname>
<given-names><![CDATA[FM]]></given-names>
</name>
<name>
<surname><![CDATA[Hamilton]]></surname>
<given-names><![CDATA[SR]]></given-names>
</name>
<name>
<surname><![CDATA[Kern]]></surname>
<given-names><![CDATA[SE]]></given-names>
</name>
<name>
<surname><![CDATA[Offerhaus]]></surname>
<given-names><![CDATA[GJA]]></given-names>
</name>
<name>
<surname><![CDATA[Green]]></surname>
<given-names><![CDATA[PA]]></given-names>
</name>
<name>
<surname><![CDATA[Celano]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Colorectal neoplasia in juvenile polyposis or juvenile polyps]]></article-title>
<source><![CDATA[Arch Dis Child]]></source>
<year>1991</year>
<volume>66</volume>
<page-range>971-5</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Sachatello]]></surname>
<given-names><![CDATA[CR]]></given-names>
</name>
<name>
<surname><![CDATA[Hahn]]></surname>
<given-names><![CDATA[IS]]></given-names>
</name>
<name>
<surname><![CDATA[Carrington]]></surname>
<given-names><![CDATA[CB]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Juvenile gastrointes tinal polyposis in a female infant: report of a case and review of the literature of a recently recognized syndrome]]></article-title>
<source><![CDATA[Surgery]]></source>
<year>1974</year>
<volume>75</volume>
<page-range>107-14</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Coburn]]></surname>
<given-names><![CDATA[MC]]></given-names>
</name>
<name>
<surname><![CDATA[Pricolo]]></surname>
<given-names><![CDATA[VE]]></given-names>
</name>
<name>
<surname><![CDATA[DeLuca]]></surname>
<given-names><![CDATA[FG]]></given-names>
</name>
<name>
<surname><![CDATA[Bland]]></surname>
<given-names><![CDATA[KI]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Malignant potential in intestinal juvenile polyposis syndromes]]></article-title>
<source><![CDATA[Ann Surg Oncol]]></source>
<year>1995</year>
<volume>2</volume>
<page-range>386-91</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Höfting]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Pott]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Stolte]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[The syndrome of juvenile polypo sis]]></article-title>
<source><![CDATA[Leber Magen Darm]]></source>
<year>1993</year>
<volume>23</volume>
<page-range>107-8</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
