<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1812-9528</journal-id>
<journal-title><![CDATA[Memorias del Instituto de Investigaciones en Ciencias de la Salud]]></journal-title>
<abbrev-journal-title><![CDATA[Mem. Inst. Investig. Cienc. Salud]]></abbrev-journal-title>
<issn>1812-9528</issn>
<publisher>
<publisher-name><![CDATA[Instituto de Investigaciones en Ciencias de la Salud]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1812-95282025000100602</article-id>
<article-id pub-id-type="doi">10.18004/mem.iics/1812-9528/2025.e23162502</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Revisión de Alcance sobre Enfermedades Priónicas: Diagnóstico y Manejo de la Enfermedad de Creutzfeldt-Jakob en humanos]]></article-title>
<article-title xml:lang="en"><![CDATA[Scope Review on Prion Diseases: Diagnosis and Management of Creutzfeldt-Jakob in Humans]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Marín-Ortega]]></surname>
<given-names><![CDATA[Cristhian Gabriel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Dr. Domingo Guzmán Lander  ]]></institution>
<addr-line><![CDATA[Barcelona Anzoátegui]]></addr-line>
<country>Venezuela</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<volume>23</volume>
<numero>1</numero>
<fpage>602</fpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_arttext&amp;pid=S1812-95282025000100602&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_abstract&amp;pid=S1812-95282025000100602&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_pdf&amp;pid=S1812-95282025000100602&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN Las enfermedades priónicas son trastornos neurodegenerativos fatales causados por proteínas anómalas, presentando 27.872 casos en 34 países entre 1993 y 2020, destacando por su progresión rápida y la falta de tratamientos efectivos, lo que plantea desafíos significativos en la atención médica. Analizar las características clínicas, los métodos de diagnóstico y las estrategias de manejo de las enfermedades priónicas, con enfoque en la Enfermedad de Creutzfeldt-Jakob, para mejorar la comprensión y el tratamiento de estas patologías neurodegenerativas. Se realizó una búsqueda sistemática en PubMed, Scielo y Dialnet para analizar las características clínicas, diagnóstico y manejo de las enfermedades priónicas. Se incluyeron estudios relevantes y se enfatizó la importancia de un enfoque multidisciplinario. Se identificaron 272 artículos; tras evaluación, 47 se incluyeron en la revisión final. Se destacan avances en el diagnóstico, uso de biomarcadores y técnicas de imagen, mejorando la detección temprana. Sin embargo, persisten desafíos en el manejo, con tratamientos sintomáticos y cuidados paliativos. Las enfermedades priónicas, debido a su naturaleza neurodegenerativa y falta de tratamientos curativos, presentan desafíos únicos en cuanto a su diagnóstico y manejo. Las características clínicas requieren un enfoque multidisciplinario para su diagnóstico temprano y el desarrollo de estrategias terapéuticas efectivas.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Prion diseases are fatal neurodegenerative disorders caused by abnormal proteins, presenting 27,872 cases in 34 countries between 1993 and 2020, notable for their rapid progression and lack of effective treatments, posing significant challenges in medical care. To analyze the clinical characteristics, diagnostic methods and management strategies of prion diseases, with a focus on Creutzfeldt-Jakob disease. A systematic search was conducted in PubMed, Scielo and Dialnet databases. Relevant studies were included and the importance of a multidisciplinary approach was emphasized. 272 articles were identified; after evaluation, 47 were included in the final review. Advances in diagnosis, use of biomarkers and imaging techniques are highlighted. However, management challenges remain, with symptomatic treatment and palliative care. Prion diseases present unique diagnostic and management challenges. The clinical features require a multidisciplinary approach for early diagnosis and the development of effective therapeutic strategies.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Priones]]></kwd>
<kwd lng="es"><![CDATA[Proteínas Priónicas]]></kwd>
<kwd lng="es"><![CDATA[Enfermedades por Prion]]></kwd>
<kwd lng="es"><![CDATA[Enfermedad de Creutzfeldt-Jakob]]></kwd>
<kwd lng="en"><![CDATA[Prions]]></kwd>
<kwd lng="en"><![CDATA[Prion Proteins]]></kwd>
<kwd lng="en"><![CDATA[Prion Diseases]]></kwd>
<kwd lng="en"><![CDATA[Creutzfeldt-Jakob Disease]]></kwd>
</kwd-group>
</article-meta>
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