<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2413-4341</journal-id>
<journal-title><![CDATA[Revista Paraguaya de Reumatología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. parag. reumatol.]]></abbrev-journal-title>
<issn>2413-4341</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Paraguaya de Reumatología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2413-43412020000200060</article-id>
<article-id pub-id-type="doi">10.18004/rpr/2020.06.02.60</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Características clínicas y mortalidad de los pacientes con vasculitis sistémica]]></article-title>
<article-title xml:lang="en"><![CDATA[Clinical characteristics and mortality of patients with vasculitis systemic]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Montiel]]></surname>
<given-names><![CDATA[Dora]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sobarzo]]></surname>
<given-names><![CDATA[Patricia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Centurión]]></surname>
<given-names><![CDATA[Claudia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Montiel]]></surname>
<given-names><![CDATA[Carmen]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Torres]]></surname>
<given-names><![CDATA[Raquel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Nacional Departamento de Medicina Interna ]]></institution>
<addr-line><![CDATA[Itaugua ]]></addr-line>
<country>Paraguay</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad Nacional de Asunción Facultad de Ciencias Médicas Hospital de Clínicas, I Cátedra de Clínica Médica]]></institution>
<addr-line><![CDATA[San Lorenzo ]]></addr-line>
<country>Paraguay</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad Nacional de Asunción Facultad de Ciencias Médicas Hospital de Clínicas, II Cátedra de Clínica Médica]]></institution>
<addr-line><![CDATA[San Lorenzo ]]></addr-line>
<country>Paraguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<volume>6</volume>
<numero>2</numero>
<fpage>60</fpage>
<lpage>69</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_arttext&amp;pid=S2413-43412020000200060&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_abstract&amp;pid=S2413-43412020000200060&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_pdf&amp;pid=S2413-43412020000200060&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  Las vasculitis sistémicas pertenecen a un grupo de enfermedades multisistémicas graves, raras, que sin tratamiento pueden poner en peligro la vida.  Objetivos:  determinar las características clínicas y mortalidad de pacientes con vasculitis sistémica, internados en el periodo comprendido entre enero de 2000 y agosto de 2020, en dos hospitales públicos de Paraguay.  Material y Método:  estudio observacional, descriptivo, retrospectivo, de corte transverso, con componente analítico, de 41 pacientes adultos, con el diagnóstico de vasculitis sistémica, internados en dos hospitales públicos de Paraguay. El diagnóstico se realizó por la clínica, laboratorio, imagen y hallazgos histológicos. Se establecieron los factores de riesgo para la mortalidad por la prueba de chi cuadrado, considerándose significativo un valor p menor de p&lt;0,05.  Resultados: Fueron estudiados 41 pacientes, 24 mujeres (58,54%) y 17 varones (41,46%), encontrando vasculitis asociadas a ANCA en 31 casos (77,5%), 17 con granulomatosis con poliangeitis y 14 pacientes con poliarteritis microscópica. Poliarteris nodosa 5 (12,5%), crioglubulinemia 2 (5%), enfermedad por anticuerpo anti membrana basal glomerular 2 (5%), arteritis de Takayasu 3 (7,32). Se encontró una mortalidad del 39%. Los factores relacionados con la mortalidad fueron: hemorragia alveolar, injuria renal aguda, nefritis rápidamente progresiva, infiltrado algodonoso bilateral (p=&#8804; 0,05).  Conclusión: La vasculitis más frecuente fue la asociada al ANCA, seguida por la parteritis nodosa. Encontramos una tasa elevada de mortalidad, secundaria sobre todo a afectación pulmonar y renal.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Systemic vasculitis belongs to a group of rare, serious multisystemic diseases, that without treatment can be life-threatening.  Objective:  To study and to determine the clinical characteristics and mortality of patients with systemic vasculitis admitted in the period 2000-2020, in two public hospitals in Paraguay.  Material and Method:  a retrospective, descriptive, observational, cross-sectional study with an analytical component of 41 adult patients with a diagnosis of systemic vasculitis. The diagnosis was made by clinical, laboratory, imaging and histological findings. Risk factors for mortality were established by the chi-square test, considering a p value less than p &lt;0.05 to be significant.  Results : 41 patients were studied, 24 women (58.54%) and 17 men (41.46%), vasculitis associated with ANCA 31 (77.5%), 17 with granulomatosis with polyangiitis and 14 patients with microscopic polyangiitis. Polyarteritis nodosa 5 (12.5%), cryoglobulinemia 2 (5%), anti-glomerular basement membrane antibody disease 2 (5%), Takayasu arteritis 3 (7.32%), progression to chronic kidney disease 5 (12.50 %)). Mortality 16 (39%). The factors related to mortality were: alveolar hemorrhage, acute kidney injury, rapidly progressive nephritis, bilateral cottony infiltrate (p = &#8804; 0.05).  Conclusion:  The most frequent vasculitis was associated with ANCA, followed by parteritis nodosa. We found a high mortality rate, mainly secondary to lung and kidney involvement.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[vasculitis sistémica]]></kwd>
<kwd lng="es"><![CDATA[vasculitis asociadas a ANCA]]></kwd>
<kwd lng="es"><![CDATA[mortalidad]]></kwd>
<kwd lng="en"><![CDATA[systemic vasculitis]]></kwd>
<kwd lng="en"><![CDATA[ANCA-associated vasculitis]]></kwd>
<kwd lng="en"><![CDATA[mortality]]></kwd>
</kwd-group>
</article-meta>
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