<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2413-4341</journal-id>
<journal-title><![CDATA[Revista Paraguaya de Reumatología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. parag. reumatol.]]></abbrev-journal-title>
<issn>2413-4341</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Paraguaya de Reumatología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2413-43412018000200052</article-id>
<article-id pub-id-type="doi">10.18004/rpr/2018.04.02.52-57</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Poliarteritis nodosa sistémica y cutánea en niños]]></article-title>
<article-title xml:lang="en"><![CDATA[Systemic and cutaneous polyarteritis nodosa in children]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Morel]]></surname>
<given-names><![CDATA[Zoilo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Melgarejo]]></surname>
<given-names><![CDATA[Patricia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Franco]]></surname>
<given-names><![CDATA[Marco]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Delgadillo]]></surname>
<given-names><![CDATA[Pedro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Instituto de Previsión Social Servicio de Reumatología ]]></institution>
<addr-line><![CDATA[Asunción ]]></addr-line>
<country>Paraguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2018</year>
</pub-date>
<volume>4</volume>
<numero>2</numero>
<fpage>52</fpage>
<lpage>57</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_arttext&amp;pid=S2413-43412018000200052&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_abstract&amp;pid=S2413-43412018000200052&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_pdf&amp;pid=S2413-43412018000200052&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN La Poliarteritis Nodosa (PAN) se define como la arteritis necrotizante de arterias de mediano y pequeño calibre, sin glomerulonefritis o vasculitis en arteriolas, capilares o vénulas, y sin asociación a anticuerpos anticitoplasma de neutrófilos (ANCA). La PAN es más frecuente en adultos, con igual presentación en ambos sexos. Se presenta el caso de un niño de 13 años de edad, con fiebre prolongada, artralgias, miositis, edema de miembros inferiores, lesiones petequiales y equimóticas generalizadas, trombosis venosa profunda en pierna izquierda, isquemia con posterior necrosis del dedo pulgar izquierdo, con diagnóstico de PAN sistémica; recibió tratamiento con corticoides, IGIV y ciclofosfamida, con mejoría clínica y posterior alta. El segundo caso corresponde a un varón de 9 años de edad, con cuadro de fiebre, dolor abdominal, náuseas, vómitos, nódulos palpables y petequias en miembros inferiores y superiores, livedo reticularis en miembros inferiores, artritis en tobillos, con diagnóstico de PANc, habiendo recibido solamente corticoides, con excelente evolución.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Polyarteritis Nodosa (PAN) is defined as necrotizing arteritis of medium or small arteries without glomerulonephritis or vasculitis in arterioles, capillaries, or venules, and not associated with antineutrophil cytoplasmic antibodies (ANCA). PAN is more frequent in adults, with the same presentation in both genders. We present the case of a 13-year-old boy with prolonged fever, arthralgias, myositis, lower limb edema, generalized petechial and ecchymotic lesions, deep vein thrombosis in the left leg, ischemia with subsequent necrosis of the left thumb, with diagnosis of systemic PAN; He received treatment with corticosteroids, IVIG and cyclophosphamide, with clinical improvement. The second case corresponds to a 9-year-old male, with acute fever, abdominal pain, nausea, vomiting, palpable nodules and petechiae in the lower and upper limbs, livedo reticularis in the lower limbs, with diagnosis of PANc, having received only corticoids, with excellent evolution.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Vasculitis]]></kwd>
<kwd lng="es"><![CDATA[poliarteritis nodosa]]></kwd>
<kwd lng="es"><![CDATA[poliarteritis nodosa cutánea]]></kwd>
<kwd lng="es"><![CDATA[adultos]]></kwd>
<kwd lng="es"><![CDATA[niños]]></kwd>
<kwd lng="en"><![CDATA[Vasculitis]]></kwd>
<kwd lng="en"><![CDATA[polyarteritis nodosa]]></kwd>
<kwd lng="en"><![CDATA[cutaneous polyarteritis nodosa]]></kwd>
<kwd lng="en"><![CDATA[adults]]></kwd>
<kwd lng="en"><![CDATA[children.]]></kwd>
</kwd-group>
</article-meta>
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