<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1683-9803</journal-id>
<journal-title><![CDATA[Pediatría (Asunción)]]></journal-title>
<abbrev-journal-title><![CDATA[Pediatr. (Asunción)]]></abbrev-journal-title>
<issn>1683-9803</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Paraguaya de Pediatría]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1683-98032025000300220</article-id>
<article-id pub-id-type="doi">10.31698/ped.52032025009</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Tratamiento inmunosupresor combinado con terapia endovascular en un adolescente con arteritis de Takayasu. Reporte de caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Immunosuppressive treatment combined with endovascular therapy in an adolescent with Takayasu arteritis: a case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Greco]]></surname>
<given-names><![CDATA[Junior]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Villagra]]></surname>
<given-names><![CDATA[Lina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Benítez]]></surname>
<given-names><![CDATA[Oscar Amalio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Montiel]]></surname>
<given-names><![CDATA[Carla]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Morel]]></surname>
<given-names><![CDATA[Zoilo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad Nacional de Asunción Facultad de Ciencias Médicas Hospital de Clínicas]]></institution>
<addr-line><![CDATA[San Lorenzo ]]></addr-line>
<country>Paraguay</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad Nacional de Asunción Facultad de Ciencias Médicas Cátedra y Servicio de Pediatría]]></institution>
<addr-line><![CDATA[San Lorenzo ]]></addr-line>
<country>Paraguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2025</year>
</pub-date>
<volume>52</volume>
<numero>3</numero>
<fpage>220</fpage>
<lpage>225</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_arttext&amp;pid=S1683-98032025000300220&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_abstract&amp;pid=S1683-98032025000300220&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_pdf&amp;pid=S1683-98032025000300220&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  La Arteritis de Takayasu (AT) es una vasculitis de grandes vasos, que se caracteriza por inflamación granulomatosa de la Aorta y sus grandes ramas, resultando en estenosis, oclusiones, dilataciones y/o aneurismas, con presentación más severa en niños.  Reporte de caso:  Presentamos el caso de un adolescente de 16 años, con diagnóstico de estenosis valvular aórtica a los 3 años de edad. Se realizó diagnóstico de AT tipo IIb a los 13 años de edad por imágenes en Angiotomografía: disminución de la aorta a nivel del cayado y de sus ramas en sus orígenes con engrosamiento de las paredes vasculares. Además, presenta Anemia hemolítica autoinmune (AHA) e insuficiencia renal pre-renal por hipoflujo vascular secundario a la disminución del gasto cardiaco, a consecuencia de la estenosis supravalvular aórtica severa. Recibió tratamiento con corticoides, Inmunoglobulina humana IV, ciclofosfamida como inducción, además de Rituximab para la AHA, continuando en mantenimiento de la remisión con metotrexato. Se realizó cateterismo con colocación de Stent en aorta ascendente, con excelente resultado, mejorando inmediatamente la función renal ante la mejoría del flujo sanguíneo.  Discusión:  Ante la presencia de complicaciones vasculares en la AT, por afectación crónica de las mismas, es importante tener en cuenta no solo el tratamiento anti-inflamatorio, sino además, la terapéutica vascular ideal para el caso (revascularización hemodinámica vs quirúrgica).]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction: Takayasu arteritis (TA) is a large-vessel vasculitis characterized by granulomatous inflammation of the aorta and its major branches, resulting in stenosis, occlusions, dilations, and/or aneurysms, with a more severe presentation in children.  Case Report:  We present the case of a 16-year-old adolescent diagnosed with aortic valve stenosis at age 3. A diagnosis of type IIb TA was made at age 13 based on CT angiography: narrowing of the aorta at the level of the aortic arch and its branches at their origins, with thickening of the vascular walls. In addition, the patient presented with autoimmune hemolytic anemia (AHA) and pre-renal insufficiency due to decreased blood flow secondary to reduced cardiac output resulting from severe supravalvular aortic stenosis. Treatment included corticosteroids, intravenous immunoglobulin, cyclophosphamide for induction therapy, and rituximab for AHA, with continued maintenance of remission on methotrexate. Cardiac catheterization with stent placement in the ascending aorta was performed, with excellent results and immediate improvement in renal function due to increased blood flow.  Discussion: In the presence of vascular complications in Takayasu arteritis, due to chronic involvement of the arteries, it is important to consider not only anti-inflammatory treatment but also the ideal vascular therapy for the case (hemodynamic vs. surgical revascularization).]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Arteritis]]></kwd>
<kwd lng="es"><![CDATA[Takayasu]]></kwd>
<kwd lng="es"><![CDATA[endovascular]]></kwd>
<kwd lng="es"><![CDATA[stent]]></kwd>
<kwd lng="es"><![CDATA[niños]]></kwd>
<kwd lng="en"><![CDATA[Arteritis]]></kwd>
<kwd lng="en"><![CDATA[Takayasu arteritis]]></kwd>
<kwd lng="en"><![CDATA[endovascular]]></kwd>
<kwd lng="en"><![CDATA[stent]]></kwd>
<kwd lng="en"><![CDATA[children]]></kwd>
</kwd-group>
</article-meta>
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