<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1683-9803</journal-id>
<journal-title><![CDATA[Pediatría (Asunción)]]></journal-title>
<abbrev-journal-title><![CDATA[Pediatr. (Asunción)]]></abbrev-journal-title>
<issn>1683-9803</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Paraguaya de Pediatría]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1683-98032022000100027</article-id>
<article-id pub-id-type="doi">10.31698/ped.49012022005</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Caracterización de niños y adolescentes con Fibrosis Quística que acuden a un hospital de IV Nivel de Atención del Seguro Social de Paraguay, años 2016 a 2019]]></article-title>
<article-title xml:lang="en"><![CDATA[Characterization of children and adolescents with Cystic Fibrosis who present to a Level IV Social Security Hospital in Paraguay, from 2016 to 2019]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Macoritto González]]></surname>
<given-names><![CDATA[Leticia]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Florentín]]></surname>
<given-names><![CDATA[Gladys]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rios-González]]></surname>
<given-names><![CDATA[Carlos Miguel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad Nacional de Caaguazú Facultad de Ciencias Médicas ]]></institution>
<addr-line><![CDATA[Coronel Oviedo ]]></addr-line>
<country>Paraguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2022</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2022</year>
</pub-date>
<volume>49</volume>
<numero>1</numero>
<fpage>27</fpage>
<lpage>32</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_arttext&amp;pid=S1683-98032022000100027&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_abstract&amp;pid=S1683-98032022000100027&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_pdf&amp;pid=S1683-98032022000100027&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN  Introducción:  La fibrosis quística es una enfermedad que afecta a múltiples sistemas del organismo tanto de niños como de adultos. Constituye el trastorno genético limitante más frecuente de los caucásicos.  Objetivo:  Caracterizar a los pacientes con fibrosis quística (FQ)internados en el Servicio de Pediatría de un Hospital de IV Nivel de Atención del Seguro Social de Paraguay durante los años 2016 y 2019.  Materiales y Métodos:  Estudio observacional, descriptivo, de corte transversal, con muestreo no probabilístico, en niños/as que acudieron al Hospital entre los años 2016 y 2019. Se utilizaron las historias clínicas de los pacientes ingresados, que cumplieron con los criterios de inclusión.  Resultados:  Fueron incluidos 52 pacientes, 32/52 (61,54%) fueron del sexo femenino. La mediana de edad fue de 3 años (1 mes a 16 años). Del total, 37/52 (71,2%) pacientes no contaba con antecedentes familiares de FQ y el tiempo de diagnóstico que más frecuente fue entre los 0 a 8 meses de edad. La manifestación clínica al momento del diagnóstico que predominó fue la mixta (respiratorio/digestivo) en 38/52 pacientes (73,1%) y el patógeno más comúnmente aislado de secreción traqueal fue la Pseudomona aeruginosa en 33 (63,5%) de ellos. Cursaron con riesgo de desnutrición 18(34,6%) pacientes.  Conclusión:  Se pudo apreciar un predominio del sexo femenino, siendo la forma clínica de debut predominante la mixta, respiratorio y digestiva. Un tercio de los pacientes se encontraban con riesgo de desnutrición.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT  Introduction:  Cystic fibrosis is a disease that affects multiple body systems in both children and adults. It is the most common limiting genetic disorder in Caucasians.  Objective:  To characterize patients with cystic fibrosis (CF) hospitalized in the Pediatric Service of a Level IV Social Security Hospital in Paraguay during 2016-2019.  Materials and Methods:  this was an observational, descriptive and cross-sectional study, with non-probabilistic sampling, in children who presented to the Hospital between 2016 and 2019. The medical records of admitted patients who met the inclusion criteria were used.  Results:  52 patients were included, 32/52 (61.54%) were female. The median age was 3 years (1 month to 16 years). Of the total, 37/52 (71.2%) patients did not have a family history of CF and the most frequent time of diagnosis was between 0 and 8 months of age. The predominant clinical manifestation at the time of diagnosis was mixed (respiratory/digestive) in 38/52 patients (73.1%) and the most commonly isolated pathogen from tracheal secretions was Pseudomonas aeruginosa in 33 (63.5%) of them. they. 18 (34.6%) patients were at risk of malnutrition.  Conclusion:  a predominance of the female sex was observed, the predominant clinical form of debut was mixed, respiratory and digestive. One third of the patients were at risk of malnutrition.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Fibrosis Quística]]></kwd>
<kwd lng="es"><![CDATA[características]]></kwd>
<kwd lng="es"><![CDATA[desnutrición]]></kwd>
<kwd lng="en"><![CDATA[Cystic Fibrosis]]></kwd>
<kwd lng="en"><![CDATA[characteristics]]></kwd>
<kwd lng="en"><![CDATA[malnutrition]]></kwd>
</kwd-group>
</article-meta>
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