<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1683-9803</journal-id>
<journal-title><![CDATA[Pediatría (Asunción)]]></journal-title>
<abbrev-journal-title><![CDATA[Pediatr. (Asunción)]]></abbrev-journal-title>
<issn>1683-9803</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Paraguaya de Pediatría]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1683-98032020000300175</article-id>
<article-id pub-id-type="doi">10.31698/ped.47032020010</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Síndrome de Gorham Stout. Reporte de Caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Gorham Stout Syndrome. A Case Report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Domínguez Samaniego]]></surname>
<given-names><![CDATA[Sandra Violeta]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vega]]></surname>
<given-names><![CDATA[Osvaldo Guzmán]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital General Pediátrico &#8220;Niños de Acosta Ñu&#8221;  ]]></institution>
<addr-line><![CDATA[San Lorenzo ]]></addr-line>
<country>Paraguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2020</year>
</pub-date>
<volume>47</volume>
<numero>3</numero>
<fpage>175</fpage>
<lpage>179</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_arttext&amp;pid=S1683-98032020000300175&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_abstract&amp;pid=S1683-98032020000300175&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_pdf&amp;pid=S1683-98032020000300175&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN El Síndrome de Gorham Stout (GSS) es una enfermedad ósea de etiología desconocida, caracterizada por osteólisis, absorción idiopática y progresiva. Se presenta a cualquier edad, sin predilección por género o raza, puede afectar cualquier parte del esqueleto, el diagnóstico que se realiza es clínico, radiológico e histopatológico y por exclusión de otras afecciones comunes. El compromiso espinal es extremadamente raro y de mal pronóstico. También afecta las vísceras, una complicación común es el desarrollo de quilotórax, que ocurre en aproximadamente 20% de los pacientes y con lleva una alta tasa de mortalidad. No existen métodos de diagnósticos o tratamientos estándar para la enfermedad. Plantea un desafío para los médicos a la hora de diagnosticar y tratar adecuadamente al paciente. Se presenta el caso de una paciente de 5 años de edad, diagnosticada y manejada por un equipo multidisciplinario en el Hospital General Pediátrico (HGP), con revisión de la literatura.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Gorham Stout Syndrome (GSS) is a bone disease of unknown etiology, characterized by idiopathic osteolysis and progressive absorption. It occurs at any age, without predilection for gender or race; it can affect any part of the skeleton, the diagnosis is clinical, radiological and histopathological and by exclusion of other common conditions. Spinal involvement is extremely rare and has a poor prognosis. It also affects the viscera, a common complication is the development of chylothorax, which occurs in approximately 20% of patients and carries a high mortality rate. There are no standard diagnostic methods or treatments for the disease. It poses a diagnostic and therapeutic challenge for clinicians. We present the case of a 5-year-old patient, diagnosed and managed by a multidisciplinary team at the Pediatric General Hospital (HGP), with a review of the literature on the topic.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Gorham Stout]]></kwd>
<kwd lng="es"><![CDATA[pediatría]]></kwd>
<kwd lng="es"><![CDATA[osteólisis]]></kwd>
<kwd lng="en"><![CDATA[Gorham Stout syndrome]]></kwd>
<kwd lng="en"><![CDATA[pediatrics]]></kwd>
<kwd lng="en"><![CDATA[osteolysis]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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