<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1683-9803</journal-id>
<journal-title><![CDATA[Pediatría (Asunción)]]></journal-title>
<abbrev-journal-title><![CDATA[Pediatr. (Asunción)]]></abbrev-journal-title>
<issn>1683-9803</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Paraguaya de Pediatría]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1683-98032017000200148</article-id>
<article-id pub-id-type="doi">10.18004/ped.2017.agosto.148-152</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Cáncer colorectal en la edad pediátrica: reporte de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Colorectal cancer in pediatric age: case report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Karim]]></surname>
<given-names><![CDATA[Aitidir]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Centro Especializado de Consulta Dirección de Servicio de Pediatría ]]></institution>
<addr-line><![CDATA[Hussein Dey Argel ]]></addr-line>
<country>Argelia</country>
</aff>
<pub-date pub-type="pub">
<day>30</day>
<month>08</month>
<year>2017</year>
</pub-date>
<pub-date pub-type="epub">
<day>30</day>
<month>08</month>
<year>2017</year>
</pub-date>
<volume>44</volume>
<numero>2</numero>
<fpage>148</fpage>
<lpage>152</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_arttext&amp;pid=S1683-98032017000200148&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_abstract&amp;pid=S1683-98032017000200148&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://scielo.iics.una.py/scielo.php?script=sci_pdf&amp;pid=S1683-98032017000200148&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[RESUMEN El cáncer colorrectal (CCR) constituye una dolencia extremadamente infrecuente en niños. Es más excepcional cuando ocurre en niños con neurofibromatosis tipo 1, que es considerada como factor de riesgo para el desarrollo de tumores malignos. Se reporta el caso de un niño de 8 años con CCR metastático de alto grado. El paciente presentó diarrea crónica muco-sanguinolenta, rectorragia y pérdida de peso. Su examen reveló manchas café con leche diseminadas sobre la espalda, pelvis y miembros inferiores. En la colonoscopia se visualizó una masa polipoide, estenosante, pediculada, ulcerativa, localizada a 35 cm del margen anal. La TAC reveló una metástasis hepática. Se realizó una colectomía amplia y el estudio histológico demostró 23 pólipos, 112 ganglios reaccionales y un tumor con componente mucinoso. Recibió quimioterapia y lobectomía hepática. No hay protocolo específico para el tratamiento de esta afección en niños. El pronóstico depende principalmente del carácter agresivo del tumor, de su estadificación y del lugar en el que se desarrolla.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[ABSTRACT Colorectal cancer (CRC) is an extremely rare condition in children. It is more exceptional when it oc-curs in children with neurofibromatosis type 1, which is considered a risk factor for the development of malignant tumors. We report the case of an 8-year-old child with high-grade metastatic CRC. The patient had chronic muco-bloody diarrhea, rectal bleeding and weight loss. His examination revealed cafe-au-lait spots scattered on his back, pelvis, and lower limbs. A polipoid, stenosing, pediculated, ul-cerative mass located 35 cm from the anal margin was visualized by colonoscopy. CT revealed hepatic metastasis. An ample colectomy was performed and the histology showed 23 polyps, 112 reactive lymph nodes and one tumor with a mucinous component. The patient received chemotherapy and liver lobectomy. There is no specific protocol for the treatment of this condition in children. The prog-nosis depends mainly on the aggressive nature of the tumor, its staging and the place where it develops.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Adenocarcinoma colorrectal]]></kwd>
<kwd lng="es"><![CDATA[neurofibromatosis]]></kwd>
<kwd lng="es"><![CDATA[niños]]></kwd>
<kwd lng="es"><![CDATA[mucinoso]]></kwd>
<kwd lng="es"><![CDATA[pronóstico]]></kwd>
<kwd lng="en"><![CDATA[Colorectal adenocarcinoma]]></kwd>
<kwd lng="en"><![CDATA[neurofibromatosis]]></kwd>
<kwd lng="en"><![CDATA[children]]></kwd>
<kwd lng="en"><![CDATA[mucinous]]></kwd>
<kwd lng="en"><![CDATA[prognosis]]></kwd>
</kwd-group>
</article-meta>
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