Abstract

FERNANDEZ, Claudia María; GOMEZ, Clara Giselle  and  SIRTORI, María Romina. Aggressive pelvic angiomyxoma. A case report. An. Fac. Cienc. Méd. (Asunción) [online]. 2021, vol.54, n.2, pp.131-136. ISSN 1816-8949.  https://doi.org/10.18004/anales/2021.054.02.131.

Aggressive angiomyxoma of the pelvic floor is a rare mesenchymal neoplasm of benign histology, but with a characteristic locally aggressive behavior, which mostly occurs in women of reproductive age. It usually presents an insidious growth from its origin in the perineal musculature, which leads to a non-specific, subtle and generally long-lasting clinical course. Diagnostic imaging, mainly at the expense of CT and MRI with contrast, is of notable importance, both for allowing detection and reliable characterization of a rare entity, and for facilitating adequate surgical planning to obtain disease-free resection margins, even in those with infiltration of neighboring structures. We present the case of an adolescent patient with a history of tumor in the right vulvar region, which imaging studies confirmed to be the extension of a large retroperitoneal tumor whose pathological anatomy describes as an aggressive pelvic an angiomyxoma.

Keywords : Aggressive angiomyxoma; Pelvic tumor; Bartholin's cyst; Vulva..

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